Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 2019 , Vol 10, Issue 1
Anesthetic Management of Scoliosis Surgery For a Patient With Joubert Syndrome: a Case Report
Mehmet Bilhan Hayırlıoğlu1,Banu Gökay Vural1,Müzeyyen İyigün1,Tayfun Güler1
1Acıbadem Üniversitesi, Atakent Hastanesi, İstanbul, Türkiye DOI : 10.31067/0.2019.113 Joubert Syndrome is a rare, autosomal recessive (AR) disorder characterized byneurologic findings as hypotonia, ataxia, physhcomotor developmental delay, abnormal respiratory pattern and abnormal eye movements. Molar tooth sign caused by cerebellar vermis hypoplasia is a neuroradiologic diagnostic criteria in cranial magnetic resonance imaging (MRI). Scolisosis is common in these patients due to hypotonia during the early developmental period. In this article we presented our anesthesia management during scoliosis correction surgery in a patient with Joubert Syndrome. Keywords : Joubert syndrome, scoliosis, pediatric anesthesia, neurophysiological monitoring, neuromonitoring