Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 2011 , Vol 2, Issue 1
Pancreatoblastoma: a Rare Neoplasm of Childhood
Ali Türk1, Özlem Saygılı1, Ulaş Can2, Tuğrul Örmeci2, İnci Ayan3
1Acıbadem Üniversitesi Tıp Fakültesi, Radyoloji Anabilim Dalı, İstanbul, Türkiye
2Acıbadem Bakırköy Hastanesi, Radyoloji Bölümü, İstanbul, Türkiye
3Acıbadem Üniversitesi Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, İstanbul, Türkiye
Pancreatoblastoma is a very rare neoplasm of pancreatic origin in children. Although it is the most common pancreatic tumor in children, there are only 100 cases presented in the literature. We present a case of pancreatoblastoma discussing various radiologic imaging findings on the ultrasonography of a 4 year old girl with a complaint of left upper quadrant palpable mass. There was a large heterogenous mass with cystic necrotic areas and coarse calcifications. On CT and MRI the tumor origin was seen to be located in pancreatic body and tail. There were also metastatic liver lesions. After histopathologic diagnosis of pancreatoblastoma complete excision of the primary tumor and hepatic metastasis were performed followed by postsurgery chemotheraphy. Although it is a rare neoplasm pancreatoblastoma should be considered in the differential diagnosis of upper abdominal masses in children. Keywords : pancreatoblastoma, neoplasm, CT, MRI, US