Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 2018 , Vol 9, Issue 1
Staged Total Correction In a Child With Complex Heart Anomaly Associated With Protein C Deficiency
Dilek Suzan1, Selim Aydın1, Barış Kırat2, İbrahim Halil Demir3, Ender Ödemiş3, Ersin Erek1
1Acıbadem Üniversitesi Atakent Hastanesi, Kalp ve Damar Cerrahisi, İstanbul, Türkiye
2Acıbadem Üniversitesi Atakent Hastanesi, Anesteziyoloji ve Reanimasyon, İstanbul, Türkiye
3Acıbadem Üniversitesi Atakent Hastanesi, Çocuk Kardiyolojisi, İstanbul, Türkiye
Patients with pre-existing coagulopathies who undergo cardiac surgery are at increased risk for bleeding and thrombosis. In this study we report a staged Rastelli operation in a 4 year old child with complex congenital cardiac anomaly associated with protein C deficiency which was diagnosed due to early shunt thrombosis after modified BT shunt operation, when the patient was 1.5 years old. During 2.5 years follow-up shunt was open under anticoagulan and antiaggregant treatment. When the patient was 4 years old, Rasteli operation was performed successfully Our aim by sharing this case is to emphasize the importance of predispozing risk factors in patients with thromboembolic events after cardiac surgery. Keywords : Protein C deficiency, cardiopulmonary bypass, thrombosis, complex congenital heart defects